Rim na sindrome de Mayer-Rokitansky-Küster-Hauser

Giovanni Luis Breda, Henrique Guesser Ascenço, Maurício Carvalho

Resumo


A síndrome de Mayer-Rokitansky-Küster-Hauser (MRKH) é afecção rara, caracterizada por agenesia congênita de terço superior da vagina e ausência ou atresia uterina. Sua prevalência varia de 1:4000 a 5000 nascimentos de bebês do sexo feminino. Associa-se frequentemente a outras alterações, como anomalias renais ou malformações esqueléticas. Neste relato apresentamos uma paciente com síndrome de MRKH, nefrectomizada por provável displasia renal, com hipercalciúria e litíase em rim único.


Palavras-chave


Anormalidades congênitas; hipercalciúria; nefrolitíase

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Referências


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DOI: http://dx.doi.org/10.5380/rmu.v1i1.40685

DOI (PDF): http://dx.doi.org/10.5380/rmu.v1i1.40685.g24932

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